A Case of Jeavons Syndrome: Eyelid Myoclonus with Myoclonus Status

Published

2022-10-31

DOI:

https://doi.org/10.55229/ijbs.v25i2.13

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Authors

  • Zeba Khan Department of Psychiatry, Jawaharlal Nehru Medical college and hospital, Aligarh, U.P., India
  • Nayab Anjum Department of Psychiatry, Jawaharlal Nehru Medical college and hospital, Aligarh, U.P., India
  • M Reyazuddin Department of Psychiatry, Jawaharlal Nehru Medical college and hospital, Aligarh, U.P., India

Abstract

Jeavons initially explained Jeavons syndrome or eyelid myoclonus with or without absence in 1977.1 It has not yet been acknowledged as a categorical epileptic syndrome.2 The electroclinical trinity of photosensitivity, eye closure-induced seizures, and electroencephalography (EEG) paroxysms serve this disease’s hallmarks.3 The normal onset occurs in childhood, peaks between the ages of 2 and 14, and is more prevalent in women (F:M= 2-3:1).4
Repetitive episodes of eyelid jerking, along with eye upward deviation and head retropulsion, constitute the symptoms.5 A limited minority of patients may have eyelid myoclonus status; seizures are frequent and brief, occurring hundreds of times each day. It is known as eyelid myoclonus with absence (EMA) when it occurs in conjunction with a loss of consciousness.

How to Cite

Khan, Z., Anjum, N., & Reyazuddin, M. (2022). A Case of Jeavons Syndrome: Eyelid Myoclonus with Myoclonus Status. Indian Journal of Behavioural Sciences, 25(02), 155–157. https://doi.org/10.55229/ijbs.v25i2.13

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References

Jeavons PM. Nosological problems of myoclonic epilepsies in childhood and adolescence. Dev Med Child Neurol 1977;19:3–8. https://doi.org/10.1111/j.1469- 8749.1977.tb08014.x.

] Koutroumanidis M, Arzimanoglou A, Caraballo R, Goyal S, Kaminska A, Laoprasert P, et al. The role of EEG in the diagnosis and classification of the epilepsy syndromes: a tool for clinical practice by the ILAE Neurophysiology Task Force (Part 1). Epileptic Disord 2017;19:233–98. https://doi.org/10.1684/ epd.2017.0935.

] Covanis A. Jeavons syndrome – updated review. J Epileptol 2015;23(2):113–23. https://doi.org/10.1515/joepi-2015-0033.

] Striano S, Striano P, Nocerino C, Boccella P, Bilo L, Meo R, et al. Eyelid myoclonia with absences: an overlooked epileptic syndrome? Neurophysiol Clin 2002;32: 287–96. https://doi.org/10.1016/s0987-7053(02)00343-x.

] Panayiotopoulos CP. Jeavons syndrome. In: Panayiotopoulos CP, editor. A clinical guide to epileptic syndromes and their treatment. Based on the ILAE classifications and pratice parameters guilines. 2nd. Springer; 2010. p. 513–7

Panayiotopoulos CP. Syndromes of idiopathic generalized epilepsies not recognized by the international league against epilepsy. Epilepsia. (2005) 46(Suppl. 9):57–66. doi: 10.1111/j.1528-1167.2005.00314.x

Viravan S, Go C, Ochi A, Akiyama T, Carter Snead 3rd O, Otsubo H. Jeavons syndrome existing as occipital cortex initiating generalized epilepsy. Epilepsia. (2011) 52:1273–9. doi: 10.1111/j.1528-1167.2011.03068.x

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